Glutaric Aciduria (GA1)

Glutaric Aciduria (GA1)

The ‘building blocks’ of protein are called amino acids. In GA1, due to the lack of an enzyme, the body cannot properly deal with two of the amino acids, lysine and tryptophan. People with GA1 therefore need to restrict the amount of protein they eat.

The management of GA1 may involve the use of protein substitutes. Protein substitutes for GA1 provide all the amino acids found in protein but no lysine and only a small quantity of tryptophan. As such, they provide a source of protein that is free from, or low in, the amino acids that cause problems in GA1. If used, protein substitutes are used alongside the individual’s allowance of regular dietary protein.

Navamedic offers a range of age-specific, lifestyle-friendly and palatable protein substitutes for GA1 from the producer Vitaflo®

GA express®

GA express®

A food for special medical purposes. GA express is an unflavoured powdered lysine free, low tryptophan protein substitute containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements. GA express is for use in the dietary management of Glutaric Aciduria Type 1 (GA1) from 3 years of age

GA amino5™

GA amino5™

A powdered amino acid supplement for use in the dietary management of Glutaric Aciduria Type 1 (GA1). GA amino5 can be used as the protein component of a bespoke modular feed or in acute emergency management, if required. GA amino5 is suitable from 3 years of age. GA amino5 is a food for special medical purposes and must be used under medical supervision.

GA explore5™

GA explore5™

A powdered protein substitute for the dietary management of Glutaric Aciduria Type 1 (GA). GA explore5 is a second stage protein substitute easily made up to a smooth spoonable consistency. Suitable from 6 months of age, this is a simple choice when introducing solids. GA explore5 is a food for special medical purposes and must be used under medical supervision

GA gel™

GA gel™

A food for special medical purposes. GA gel is an unflavoured, powdered lysine free and low tryptophan protein substitute, containing essential and non essential amino acids, carbohydrate, vitamins, minerals and trace elements. GA gel is for use in the dietary management of Glutaric Aciduria Type 1 (GA1) from 6 months to 10 years of age.