healthcare professionals
Maple Syrup Urine Disease (MSUD)

The ‘building blocks’ of protein are called amino acids. In MSUD, due to the lack of an enzyme, the body cannot properly deal with three amino acids, leucine, isoleucine and valine – collectively known as the branched chain amino acids (BCAAs). People with MSUD therefore need to severely restrict the amount of protein they eat.
A key element in the management of MSUD is the use of protein substitutes. Protein substitutes for MSUD provide all the amino acids found in protein but no leucine, isoleucine or valine. In combination with the small allowance of regular dietary protein, protein substitutes ensure that an individual with MSUD has an adequate intake of protein.

Navamedic offers a range of age-specific, lifestyle-friendly and palatable protein substitutes for MSUD from the producer Vitaflo®

 

MSUD explore5™

A powdered protein substitute for the dietary management of Maple Syrup Urine Disease (MSUD).
MSUD explore5 is a second stage protein substitute easily made up to a smooth spoonable consistency. Suitable from 6 months of age, this is a simple choice when introducing solids.
MSUD explore5 is a food for special medical purposes and must be used under medical supervision

MSUD EXPLORE DATACARD

MSUD gel™

A food for special medical purposes.
MSUD gel™ is an unflavoured, powdered leucine, isoleucine and valine free protein substitute containing essential and non essential amino acids, carbohydrate, vitamins, minerals and trace elements. MSUD gel is easily made up to a smooth semi‐solid consistency. Suitable from 6 months of age, this is a simple choice for weaning onto a second stage protein substitute.

MSUD gel Datacard

MSUD express®

A food for special medical purposes.
MSUD express is a range of unflavoured, powdered leucine, isoleucine and valine free protein substitute, containing essential and non essential amino acids, carbohydrate, sugar, vitamins, minerals and trace elements.
MSUD express can be easily made to an individual’s preferred volume and is suitable from 3 years of age.

MSUD-express Datacard

MSUD cooler®

A food for special medical purposes.
MSUD cooler is a ready-to-drink, leucine, isoleucine and valine free protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and the omega-3 long chain polyunsaturated fatty acids (LCPs); docosa-hexaenoic acid (DHA) and eicosapentaenoic (EPA). With sugar and sweeteners. Available in a choice of flavours.
MSUD cooler is suitable from 3 years of age.

MSUD-cooler-Datacard

 

MSUD amino5™

A powdered amino acid supplement for use in the dietary management of Maple Syrup Urine Disease (MSUD). MSUD amino5 can be used as the protein component of a bespoke modular feed or in acute emergency management, if required. MSUD amino5 is suitable from 3 years of age.

MSUD amino5 is a food for special medical purposes and must be used under medical supervision.

MSUD animo5 Datacard