Phenylketonuria

Phenylketonuria

The ‘building blocks’ of protein are called amino acids. In PKU, due to the lack of an enzyme, the body cannot properly deal with one of the amino acids, phenylalanine. People with PKU therefore need to severely restrict the amount of protein they eat.

A key element in the management of PKU is the use of protein substitutes. Protein substitutes for PKU provide all the amino acids found in protein but no phenylalanine. In combination with the small allowance of regular dietary protein, protein substitutes ensure that an individual with PKU has an adequate intake of protein.

PKU sphere® liquid

PKU sphere® liquid

A ready-to-drink low phenylalanine* (Phe) medical food for use in the dietary management of Phenylketonuria.

PKU gel™

PKU gel™

PKU gel™ is a powdered phenylalanine free, protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements. With sugar and sweeteners. Available in a choice of flavours.

PKU express™ plus

PKU express™ plus

PKU express plus is a powdered phenylalanine free* protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and docosahexaenoic acid (DHA). Available in a choice of flavours. Flavoured options: with sugar and sweeteners. PKU express plus is for the dietary management of Phenylketonuria (PKU) from 3 years onwards. Flavour options: Unflavored, lemon, orange, tropical and raspberry.

PKU explore™

PKU explore™

A powdered protein substitute for the dietary management of Phenylketonuria (PKU). PKU explore is a second stage protein substitute easily made up to a smooth spoonable consistency. Suitable from 6 months of age, this is a simple choice when introducing solids. PKU explore is a food for special medical purposes and must be used under medical supervision.

PKU start™

PKU start™

PKU start is an amino acid based powdered phenylalanine free* formula containing other essential and non‐essential amino acids, carbohydrate, fat, vitamins, minerals, trace elements, arachidonic acid (ARA) and docosahexanoic acid (DHA). PKU start is suitable for the dietary management of Phenylketonuria from birth.

PKU squeezie®

PKU squeezie®

A ready to feed protein substitute for the dietary management of Phenylketonuria. This is a simple choice for weaning onto a second stage protein substitute and is suitable from 6 months of age. PKU squeezie is a food for special medical purposes and must be used under medical supervision.

PKU sphere™

PKU sphere™

A powdered protein substitute for the dietary management of Phenylketonuria. PKU sphere is Vitaflo’s first glycomacropeptide (GMP) based protein substitute and is suitable from 4 years of age. PKU sphere has a GMP-dominant protein source supplemented with amino acids, bringing patients the potential benefits of GMP without any compromise in nutritional profile. PKU sphere can easily be made to an individual’s preferred volume.

PKU air®

PKU air®

The lowest calorie ready to drink protein substitute for the dietary management of Phenylketonuria (PKU). PKU air is specifically designed with the needs of teenagers and adults in mind; however, it is suitable from 3 years of age. PKU air is a food for special medical purposes and must be used under medical supervision.

PKU cooler®

PKU cooler®

PKU cooler® is a ready-to-drink, phenylalanine free protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and the omega-3 long chain polyunsaturated fatty acids (LCPs); docosahexaenoic acid (DHA) and eicosapentaenoic (EPA). Contains sugar and sweeteners. Available in a choice of flavours. PKU cooler is for use in the dietary management of Phenylketonuria (PKU) from 3 years of age.

PKU express™

PKU express™

PKU express® is a powdered phenylalanine free protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements. With sugars and sweeteners. Available in a choice of flavours. PKU express can be easily made to an individual’s preferred volume and is suitable from 3 years of age.