Urea Cycle Disorders (UCD)

Urea Cycle Disorders (UCD)

The body uses protein for growth and repair. In Urea Cycle Disorders (UCDs), due to the lack of an enzyme, the body has difficulty in removing excess dietary protein from the body. People with UCDs therefore need to restrict the amount of protein they eat.

In some cases, restriction of dietary protein may lead to a shortage of essential amino acids (the building blocks of protein). The restricted diet may also lead to individuals not getting enough micronutrients (vitamins, minerals and trace elements). It may be necessary to supplement the diet with essential amino acids (EAA) and micronutrients.

Navamedic offers a range of age-specific, lifestyle-friendly and palatable protein substitutes for UCD from the producer Vitaflo®.

EAA supplement™

EAA supplement™

A powdered essential amino acid supplement for the dietary management of Urea Cycle Disorders (UCD) and other disorders of protein metabolism where essential amino acids are required. EAA supplement is suitable from 3 years of age. EAA supplement is a food for special medical purposes and must be used under medical supervision.

Basecal™

Basecal™

A protein free powder containing carbohydrate, fat (including long chain polyunsaturated fatty acids) and micronutrients for use in the dietary management of inborn errors of protein metabolism. Basecal is specifically designed to offer a more accurate and convenient method of preparing modular feeds and is suitable from 3 years of age. Basecal is a food for special medical purposes and must be used under medical supervision.

UCD amino5™

UCD amino5™

A powdered amino acid supplement for use in the dietary management of Urea Cycle Disorders (UCD). UCD amino5 can be used as the protein component of a bespoke modular feed when additional protein is required or, in acute emergency management, if required. UCD amino5 is suitable from 3 years of age. UCD amino5 is a food for special medical purposes and must be used under medical supervision.