Protein Metabolism
There are many different disorders of protein metabolism. A common factor in their management is restriction of natural dietary protein to avoid the accumulation of toxins in the body. Disorder-specific protein substitutes are used to ensure protein requirements are met.
Navamedic offers a range of age-specific, lifestyle-friendly and palatable protein substitutes for PKU from Vitaflo International Ltd. There is also support products for this area, which can typically be used in any of the protein disorders, to further help meet individual nutritional needs.
We offer products in these theraputical areas:
Phenylketonuria (PKU)
Maple Syrup Urine Disease (MSUD)
Tyrosinaemia (TYR)
Homocystinuria (HCU)
MMA/PA
Glutaric Aciduria (GA1)
Isovaleric Acidaemia (IVA)
Urea Cycle Disorders (UCD)
Support Range- Low protein Foods etc.
PKU start is an amino acid based powdered phenylalanine free* formula containing other essential and non‐essential amino acids, carbohydrate, fat, vitamins, minerals, trace elements, arachidonic acid (ARA) and docosahexanoic acid (DHA).
PKU start is suitable for the dietary management of Phenylketonuria from birth.
A powdered protein substitute for the dietary management of Phenylketonuria (PKU). PKU explore is a second stage protein substitute easily made up to a smooth spoonable consistency. Suitable from 6 months of age, this is a simple choice when introducing solids.
PKU explore is a food for special medical purposes and must be used under medical supervision.
PKU gel™ is a powdered phenylalanine free, protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements. With sugar and sweeteners. Available in a choice of flavours.
A ready to feed protein substitute for the dietary management of Phenylketonuria. This is a simple choice for weaning onto a second stage protein substitute and is suitable from 6 months of age.
PKU squeezie is a food for special medical purposes and must be used under medical supervision.
PKU express® is a powdered phenylalanine free protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements. With sugars and sweeteners. Available in a choice of flavours.
PKU express can be easily made to an individual’s preferred volume and is suitable from 3 years of age.
PKU express plus is a powdered phenylalanine free* protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and docosahexaenoic acid (DHA). Available in a choice of flavours. Flavoured options: with sugar and sweeteners. IndicationsPKU express plus is for the dietary management of Phenylketonuria (PKU) from 3 years onwards.
Flavoursoptions: Unflavored, lemon, orange, tropical and raspberry
PKU cooler® is a ready-to-drink, phenylalanine free protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and the omega-3 long chain polyunsaturated fatty acids (LCPs); docosahexaenoic acid (DHA) and eicosapentaenoic (EPA). Contains sugar and sweeteners. Available in a choice of flavours.
Indications
PKU cooler is for use in the dietary management of Phenylketonuria (PKU) from 3 years of age.
The lowest calorie ready to drink protein substitute for the dietary management of Phenylketonuria (PKU). PKU air is specifically designed with the needs of teenagers and adults in mind; however, it is suitable from 3 years of age.
PKU air is a food for special medical purposes and must be used under medical supervision.
A powdered protein substitute for the dietary management of Phenylketonuria. PKU sphere is Vitaflo’s first glycomacropeptide (GMP) based protein substitute and is suitable from 4 years of age. PKU sphere has a GMP-dominant protein source supplemented with amino acids, bringing patients the potential benefits of GMP without any compromise in nutritional profile.
PKU sphere can easily be made to an individual’s preferred volume.
PKU Sphere Liquid 20, Vanilla
DESCRIPTION
Ready-to-drink low Phenylalanine Medical Food
A blend of whey protein isolate (glycomacropeptide — GMP),
essential and non-essential amino acids, carbohydrate,
fat (including docosahexaenoic acid — DHA), vitamins
and minerals.
USE UNDER MEDICAL SUPERVISION
From 3 years of age
A powdered protein substitute for the dietary management of Maple Syrup Urine Disease (MSUD).
MSUD explore5 is a second stage protein substitute easily made up to a smooth spoonable consistency. Suitable from 6 months of age, this is a simple choice when introducing solids.
MSUD explore5 is a food for special medical purposes and must be used under medical supervision
A food for special medical purposes.
MSUD gel™ is an unflavoured, powdered leucine, isoleucine and valine free protein substitute containing essential and non essential amino acids, carbohydrate, vitamins, minerals and trace elements. MSUD gel is easily made up to a smooth semi‐solid consistency. Suitable from 6 months of age, this is a simple choice for weaning onto a second stage protein substitute.
MSUD express™ plus is an unflavoured powdered leucine, isoleucine and valine free*, protein substitute containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and docosahexaenoic acid (DHA).
Express paste – a few spoonfuls and it’s gone. Ideal for patients transitioning from gel.
Express mini drink – Low in volume. Quick to take in one go.
Express flexi drink – make up to individual’s own taste/volume. Ideal for those transitioning from a traditional protein substitute who want to make up to their own volume.
MSUD express plus is a food for special medical purposes and must be used under medical supervision.
Datacard:
A food for special medical purposes.
MSUD express is a range of unflavoured, powdered leucine, isoleucine and valine free protein substitute, containing essential and non essential amino acids, carbohydrate, sugar, vitamins, minerals and trace elements.
MSUD express can be easily made to an individual’s preferred volume and is suitable from 3 years of age.
A food for special medical purposes.
MSUD cooler is a ready-to-drink, leucine, isoleucine and valine free protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and the omega-3 long chain polyunsaturated fatty acids (LCPs); docosa-hexaenoic acid (DHA) and eicosapentaenoic (EPA). With sugar and sweeteners. Available in a choice of flavours.
MSUD cooler is suitable from 3 years of age.
A powdered amino acid supplement for use in the dietary management of Maple Syrup Urine Disease (MSUD). MSUD amino5 can be used as the protein component of a bespoke modular feed or in acute emergency management, if required. MSUD amino5 is suitable from 3 years of age.
MSUD amino5 is a food for special medical purposes and must be used under medical supervision.
A powdered protein substitute for the dietary management of Tyrosinaemia(TYR).
TYR explore5 is a second stage protein substitute easily made up to a smooth spoonable consistency. Suitable from 6 months of age, this is a simple choice when introducing solids.
TYR explore5 is a food for special medical purposes and must be used under medical supervision.
A food for special medical purposes.
TYR gel™ is an unflavoured, powdered tyrosine and phenylalanine free protein substitute, containing essential and non essential amino acids, carbohydrate, vitamins, minerals and trace elements.
Suitable from 6 months of age, this is a simple choice for weaning onto a second stage protein substitute.
For the dietary management of Tyrosinaemia
A powdered protein substitute suitable for the dietary management of Tyrosinaemia. TYR express can be easily made to an individual’s preferred volume and is suitable from 3 years of age.
TYR express plus is a food for special medical purposes and must be used under medical supervision.
TYR EXpress PLUS datacard:
A food for special medical purposes.
TYR express® is an unflavoured powdered phenylalanine and tyrosine free, protein substitute containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements. TYR express can be easily made to an individual’s preferred volume and is suitable from 3 years of age.
A food for special medical purposes.
TYR cooler is a ready-to-drink, phenylalanine and tyrosine free protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and the omega-3 long chain polyunsaturated fatty acids (LCPs); docosahexaenoic acid (DHA) and eicosapentaenoic (EPA). With sugar and sweeteners. Available in a choice of flavours.
TYR cooler is suitable from 3 years of age.
TYR cooler is a food for special medical purposes and must be used under medical supervision.
A powdered medical food for the dietary management of Tyrosinemia. TYR is Vitaflo’s GMP-based medical food with a GMP-dominant protein source supplemented with amino acids, bringing patients the potential benefit of GMP without any compromise in nutritional profile.
Suitable from 4 years of age.
TYR sphere is medical food intended for use under medical supervision.
A powdered protein substitute for the dietary management of Homocystinuria (HCU).
HCU explore5 is a second stage protein substitute easily made up to a smooth spoonable consistency. Suitable from 6 months of age, this is a simple choice when introducing solids.
HCU explore5 is a food for special medical purposes and must be used under medical supervision.
A food for special medical purposes
HCU gel™ is an unflavoured, powdered methionine free protein substitute, containing essential and non essential amino acids, carbohydrate, vitamins, minerals and trace elements
For the dietary management of Homocystinuria
A powdered protein substitute for the dietary management of Homocystinuria. HCU express PLUS can be easily made to an individual’s preferred volume and is suitable from 3 years of age.
Express PLUS paste – a few spoonfuls and it’s gone. Ideal for patients transitioning from gel. Express plus mini drink – Low in volume. Quick to take in one go.
Express PLUS flexi drink – make up to individual’s own taste/volume. Ideal for patients transitioning from a traditional protein substitute who want to make up to their own volume.
Datacard:
A food for special medical purposes.
HCU express® is an unflavoured powdered methionine free protein substitute containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements.
A food for special medical purposes.
HCU cooler is a ready-to-drink, methionine free protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and the omega-3 long chain polyunsaturated fatty acids (LCPs); docosahexaenoic acid (DHA) and eicosapentaenoic (EPA). With sugar and sweeteners. Available in a choice of flavours. HCU cooler is suitable from 3 years of age.
HCU cooler is a food for special medical purposes and must be used under medical supervision.
A powdered protein substitute for the dietary management of Methylmalonic Acidaemia and Propionic Acidaemia (MMA/PA).
MMA/PA explore5 is a second stage protein substitute easily made up to a smooth spoonable consistency. Suitable from 6 months of age, this is a simple choice when introducing solids.
MMA/PA explore5 is a food for special medical purposes and must be used under medical supervision.
A food for special medical purposes.
MMA/PA gel™ is an unflavoured, powdered methionine, threonine and valine free and low isoleucine protein substitute, containing essential and non essential amino acids, carbohydrate, vitamins, minerals and trace elements.
Indications
MMA/PA gel is for use in the dietary management of Methylmalonic Acidaemia (MMA) and Propionic Acidaemia (PA) from 6 months to 10 years of age
A food for special medical purposes.
MMA/PA express is an unflavoured powdered methionine, threonine and valine free, low isoleucine protein substitute containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements.
Indications
MMA/PA express is for use in the dietary management of Methylmalonic Acidaemia (MMA) and Propionic Acidaemia (PA) from 3 years of age.
A food for special medical purposes.
MMA/PA cooler is a ready-to-drink, methionine, threonine and valine free and low isoleucine protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and the omega-3 long chain polyunsaturated fatty acids (LCPs); docosahexaenoic acid (DHA) and eicosapentaenoic (EPA).
With sugar and sweeteners.
MMA/PA cooler is suitable from 3 years of age.
A powdered amino acid supplement for use in the dietary management of Methylmalonic acidaemia (MMA) and Propionic acidaemia (PA). MMA/PA amino5 can be used as the protein component of a bespoke modular feed or in acute emergency management, if required. MMA/PA amino5 is suitable from 3 years of age.
A powdered protein substitute for the dietary management of Glutaric Aciduria Type 1 (GA).
GA explore5 is a second stage protein substitute easily made up to a smooth spoonable consistency. Suitable from 6 months of age, this is a simple choice when introducing solids.
GA explore5 is a food for special medical purposes and must be used under medical supervision.
A food for special medical purposes.
GA gel is an unflavoured, powdered lysine free and low tryptophan protein substitute, containing essential and non essential amino acids, carbohydrate, vitamins, minerals and trace elements.
Indication
GA gel is for use in the dietary management of Glutaric Aciduria Type 1 (GA1) from 6 months to 10 years of age.
A powdered amino acid supplement for use in the dietary management of Glutaric Aciduria Type 1 (GA1). GA amino5 can be used as the protein component of a bespoke modular feed or in acute emergency management, if required. GA amino5 is suitable from 3 years of age.
GA amino5 is a food for special medical purposes and must be used under medical supervision.
A convenient, low volume, ready to drink protein substitute for the dietary management of Isovaleric Acidaemia.
IVA cooler is suitable from 3 years of age.
IVA cooler is a food for special medical purposes and must be used under medical supervision.
A powdered amino acid supplement for use in the dietary management of Urea Cycle Disorders (UCD). UCD amino5 can be used as the protein component of a bespoke modular feed when additional protein is required or, in acute emergency management, if required. UCD amino5 is suitable from 3 years of age.
UCD amino5 is a food for special medical purposes and must be used under medical supervision.
A powdered essential amino acid supplement for the dietary management of Urea Cycle Disorders (UCD) and other disorders of protein metabolism where essential amino acids are required. EAA supplement is suitable from 3 years of age.
EAA supplement is a food for special medical purposes and must be used under medical supervision.
A food for special medical purposes.
ProZero is a liquid blend of carbohydrate and fat designed as a milk replacement.
ProZero is protein free alternative and is for use in the dietary management of inborn errors of metabolism from 6 months of age.
Fate Special Foods is a small family company which produces baking mixes suitable for those on a low protein diet. It was founded by Eileen and Martin Green after their two daughters, Faye and Kate, were diagnosed with Phenylketonuria (PKU) – an inherited metabolic disorder where treatment is a medically controlled low protein diet
Fate All Purpose Mix Flour mix from Fate Foods with good baking properties.
Produktblad Fate all purpose mix
Fate chokladmix Produktdatablad
Fate Chocolate mix and Cake mix Can be ordered directly through us.
You can also order the recipe booklet at a cost – please contact Navamedic for more information.
For tips on how to use the product please visit:
Fates YouTube channel www.youtube.com/user/fatespecialfoods/videos
Or
A food for special medical purposes
Mini Crackers are low protein herb flavoured crackers in the dietary management of children from 3 years of age and adults on protein restricted diets.
Indications
Mini Crackers are for use in the dietary management of inborn errors of protein metabolism.
MINICRACKERS low-protein-crackers-Datacard
A food for special medical purposes.
Vitabite is a low protein, high energy chocolate flavoured bar.
Indications
Vitabite is suitable for use in the dietary management of inborn errors of metabolism, liver or renal disease from 1 year of age.
A food for special medical purposes.
FlavourPac are a range of powdered protein free flavours, available in blackcurrant, orange, raspberry and tropical options.
Containing carbohydrate, sugar, sweeteners and colouring.
Suitable from 3 years of age.
A great tasting, orange flavour vitamin, mineral and trace element supplement suitable for children on restrictive therapeutic diets. FruitiVits is suitable from 3 to 10 years of age.
Fruitivits is a food for special medical purposes and must be used under medical supervision.