The ‘building blocks’ of protein are called amino acids. In Methylmalonic acidaemia (MMA) and Propionic acidaemia (PA), due to a lack of specific enzymes, the body cannot properly deal with four of the amino acids, methionine, threonine , valine and isoleucine . People with MMA or PA therefore need to restrict the amount of protein they eat.
The management of MMA or PA may involve the use of protein substitutes. Protein substitutes for MMA or PA provide all the amino acids found in protein but no methionine, threonine or valine and only a small quantity of isoleucine. As such, they provide a source of protein that is free from, or low in, the amino acids that cause problems in MMA and PA. If used, protein substitutes are used alongside the individual’s allowance of regular dietary protein.
Navamedic offers a range of age-specific, lifestyle-friendly and palatable protein substitutes for MMA and PA from the producer Vitaflo®
A food for special medical purposes.
MMA/PA gel™ is an unflavoured, powdered methionine, threonine and valine free and low isoleucine protein substitute, containing essential and non essential amino acids, carbohydrate, vitamins, minerals and trace elements.
Indications
MMA/PA gel is for use in the dietary management of Methylmalonic Acidaemia (MMA) and Propionic Acidaemia (PA) from 6 months to 10 years of age
A food for special medical purposes.
MMA/PA express is an unflavoured powdered methionine, threonine and valine free, low isoleucine protein substitute containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements.
Indications
MMA/PA express is for use in the dietary management of Methylmalonic Acidaemia (MMA) and Propionic Acidaemia (PA) from 3 years of age.
A food for special medical purposes.
MMA/PA cooler is a ready-to-drink, methionine, threonine and valine free and low isoleucine protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and the omega-3 long chain polyunsaturated fatty acids (LCPs); docosahexaenoic acid (DHA) and eicosapentaenoic (EPA).
With sugar and sweeteners.
MMA/PA cooler is suitable from 3 years of age.
A powdered amino acid supplement for use in the dietary management of Methylmalonic acidaemia (MMA) and Propionic acidaemia (PA). MMA/PA amino5 can be used as the protein component of a bespoke modular feed or in acute emergency management, if required. MMA/PA amino5 is suitable from 3 years of age.
A powdered protein substitute for the dietary management of Methylmalonic Acidaemia and Propionic Acidaemia (MMA/PA).
MMA/PA explore5 is a second stage protein substitute easily made up to a smooth spoonable consistency. Suitable from 6 months of age, this is a simple choice when introducing solids.
MMA/PA explore5 is a food for special medical purposes and must be used under medical supervision.