Homocystinuria

Homocystinuria

The ‘building blocks’ of protein are called amino acids. In HCU, due to the lack of an enzyme, the body cannot properly deal with one of the amino acids, methionine. People with HCU therefore need to severely restrict the amount of protein they eat.

A key element in the management of HCU is the use of protein substitutes. Protein substitutes for HCU provide all the amino acids found in protein but no methionine. In combination with the small allowance of regular dietary protein, protein substitutes ensure that an individual with HCU has an adequate intake of protein.

Navamedic offers a range of age-specific, lifestyle-friendly and palatable protein substitutes for HCU from the producer Vitaflo®

HCU cooler®

HCU cooler®

A food for special medical purposes. HCU cooler is a ready-to-drink, methionine free protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and the omega-3 long chain polyunsaturated fatty acids (LCPs); docosahexaenoic acid (DHA) and eicosapentaenoic (EPA). With sugar and sweeteners. Available in a choice of flavours. HCU cooler is suitable from 3 years of age. HCU cooler is a food for special medical purposes and must be used under medical supervision.

HCU express™

HCU express™

A food for special medical purposes. HCU express® is an unflavoured powdered methionine free protein substitute containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements.

HCU gel™

HCU gel™

A food for special medical purposes HCU gel™ is an unflavoured, powdered methionine free protein substitute, containing essential and non essential amino acids, carbohydrate, vitamins, minerals and trace elements

HCU explore5™

HCU explore5™

A powdered protein substitute for the dietary management of Homocystinuria (HCU). HCU explore5 is a second stage protein substitute easily made up to a smooth spoonable consistency. Suitable from 6 months of age, this is a simple choice when introducing solids. HCU explore5 is a food for special medical purposes and must be used under medical supervision.