healthcare professionals
Tyrosinaemia (TYR)

The ‘building blocks’ of protein are called amino acids. In Tyrosinaemia, due to the lack of an enzyme, the body cannot properly deal with one of the amino acids, tyrosine. (As the body uses another amino acid, called phenylalanine, to make tyrosine, there are also problems with excessive intakes of phenylalanine.) People with Tyrosinaemia therefore need to severely restrict the amount of protein they eat.

A key element in the management of Tyrosinaemia is the use of protein substitutes. Protein substitutes for Tyrosinaemia provide all the amino acids found in protein but no tyrosine or phenylalanine. In combination with the small allowance of regular dietary protein, protein substitutes ensure that an individual with Tyrosinaemia has an adequate intake of protein.

Navamed offers a range of age-specific, lifestyle-friendly and palatable protein substitutes for TYR from the producer Vitaflo®.

TYR explore5™

A powdered protein substitute for the dietary management of Tyrosinaemia(TYR).

TYR explore5 is a second stage protein substitute easily made up to a smooth spoonable consistency. Suitable from 6 months of age, this is a simple choice when introducing solids.

TYR explore5 is a food for special medical purposes and must be used under medical supervision.

TYR EXPLORE DATACARD

TYR gel™

A food for special medical purposes.
TYR gel™ is an unflavoured, powdered tyrosine and phenylalanine free protein substitute, containing essential and non essential amino acids, carbohydrate, vitamins, minerals and trace elements.
Suitable from 6 months of age, this is a simple choice for weaning onto a second stage protein substitute.

TYR-gel Datacard

TYR express®

A food for special medical purposes.
TYR express® is an unflavoured powdered phenylalanine and tyrosine free, protein substitute containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements.  TYR express can be easily made to an individual’s preferred volume and is suitable from 3 years of age.

TYR-express-Datacard

TYR cooler®

A food for special medical purposes.
TYR cooler is a ready-to-drink, phenylalanine and tyrosine free protein substitute, containing essential and non-essential amino acids, carbohydrate, vitamins, minerals, trace elements and the omega-3 long chain polyunsaturated fatty acids (LCPs); docosahexaenoic acid (DHA) and eicosapentaenoic (EPA). With sugar and sweeteners. Available in a choice of flavours.

TYR cooler is suitable from 3 years of age.

 

TYR cooler is a food for special medical purposes and must be used under medical supervision.

 

TYR-Cooler datacard

TYR sphere™

A powdered medical food for the dietary management of Tyrosinemia. TYR is Vitaflo’s GMP-based medical food with a GMP-dominant protein source supplemented with amino acids, bringing patients the potential benefit of GMP without any compromise in nutritional profile.

Suitable from 4 years of age.

TYR sphere is medical food intended for use under medical supervision.

TYR-sphere_datasheet